Effects of Cdh23 single nucleotide substitutions on age-related hearing loss in C57BL/6 and 129S1/Sv mice and comparisons with congenic strains KR Johnson, C Tian, LH Gagnon, H Jiang, D Ding, R Salvi Scientific reports 7 (1), 44450, 2017 | 61 | 2017 |
Loss of the E3 ubiquitin ligase LRSAM1 sensitizes peripheral axons to degeneration in a mouse model of Charcot-Marie-Tooth disease LP Bogdanik, JN Sleigh, C Tian, ME Samuels, K Bedard, KL Seburn, ... Disease Models & Mechanisms 6 (3), 780-792, 2013 | 59 | 2013 |
N-acetyl-cysteine prevents age-related hearing loss and the progressive loss of inner hair cells in γ-glutamyl transferase 1 deficient mice D Ding, H Jiang, GD Chen, C Longo-Guess, VPK Muthaiah, C Tian, ... Aging (albany NY) 8 (4), 730, 2016 | 53 | 2016 |
Sh3pxd2b Mice Are a Model for Craniofacial Dysmorphology and Otitis Media B Yang, C Tian, Z Zhang, F Han, R Azem, H Yu, Y Zheng, G Jin, JE Arnold, ... PLoS One 6 (7), e22622, 2011 | 49 | 2011 |
Role for Toll-Like Receptor 2 in the Immune Response to Streptococcus pneumoniae Infection in Mouse Otitis Media F Han, H Yu, C Tian, S Li, MR Jacobs, C Benedict-Alderfer, QY Zheng Infection and immunity 77 (7), 3100-3108, 2009 | 48 | 2009 |
A new mouse mutant of the Cdh23 gene with early-onset hearing loss facilitates evaluation of otoprotection drugs F Han, H Yu, C Tian, HE Chen, C Benedict-Alderfer, Y Zheng, Q Wang, ... The pharmacogenomics journal 12 (1), 30-44, 2012 | 45 | 2012 |
The roles of USH1 proteins and PDZ domain-containing USH proteins in USH2 complex integrity in cochlear hair cells J Zou, Q Chen, A Almishaal, PD Mathur, T Zheng, C Tian, QY Zheng, ... Human molecular genetics 26 (3), 624-636, 2017 | 44 | 2017 |
Otitis Media in a New Mouse Model for CHARGE Syndrome with a Deletion in the Chd7 Gene C Tian, H Yu, B Yang, F Han, Y Zheng, CF Bartels, D Schelling, JE Arnold, ... PLoS ONE 7 (4), e34944, 2012 | 36 | 2012 |
Otitis media in a mouse model for Down syndrome F Han, H Yu, J Zhang, C Tian, C Schmidt, C Nava, MT Davisson, ... International journal of experimental pathology 90 (5), 480-488, 2009 | 35 | 2009 |
Ush1c gene expression levels in the ear and eye suggest different roles for Ush1c in neurosensory organs in a new Ush1c knockout mouse C Tian, XZ Liu, F Han, H Yu, C Longo-Guess, B Yang, C Lu, D Yan, ... Brain research 1328, 57-70, 2010 | 31 | 2010 |
Deletion of a Long-Range Dlx5 Enhancer Disrupts Inner Ear Development in Mice KR Johnson, LH Gagnon, C Tian, CM Longo-Guess, BE Low, MV Wiles, ... Genetics 208 (3), 1165-1179, 2018 | 23 | 2018 |
Pathological Features in the< i> Lmna</i>< sup> Dhe/+</sup> Mutant Mouse Provide a Novel Model of Human Otitis Media and Laminopathies Y Zhang, H Yu, M Xu, F Han, C Tian, S Kim, E Fredman, J Zhang, ... The American Journal of Pathology, 2012 | 23 | 2012 |
Ectopic Mineralization and Conductive Hearing Loss in Enpp1asj Mutant Mice, a New Model for Otitis Media and Tympanosclerosis C Tian, BS Harris, KR Johnson PloS one 11 (12), e0168159, 2016 | 22 | 2016 |
A novel long intergenic non-coding RNA, Nostrill, regulates iNOS gene transcription and neurotoxicity in microglia NW Mathy, O Burleigh, A Kochvar, ER Whiteford, M Behrens, P Marta, ... Journal of neuroinflammation 18, 1-18, 2021 | 21 | 2021 |
Mutation in Phex Gene Predisposes BALB/c-PhexHyp-Duk/Y Mice to Otitis Media F Han, H Yu, P Li, J Zhang, C Tian, H Li, QY Zheng Public Library of Science 7 (9), e43010, 2012 | 17 | 2012 |
Detecting novel ototoxins and potentiation of ototoxicity by disease settings AB Coffin, R Boney, J Hill, C Tian, PS Steyger Frontiers in neurology 12, 725566, 2021 | 16 | 2021 |
Hearing loss without overt metabolic acidosis in ATP6V1B1 deficient MRL mice, a new genetic model for non-syndromic deafness with enlarged vestibular aqueducts C Tian, LH Gagnon, C Longo-Guess, R Korstanje, SM Sheehan, ... Human molecular genetics 26 (19), 3722-3735, 2017 | 14 | 2017 |
TBX1 is required for normal stria vascularis and semicircular canal development C Tian, KR Johnson Developmental biology 457 (1), 91-103, 2020 | 13 | 2020 |
Spontaneous mutations of the Zpld1 gene in mice cause semicircular canal dysfunction but do not impair gravity receptor or hearing functions S Vijayakumar, SM Jones, TA Jones, C Tian, KR Johnson Scientific reports 9 (1), 12430, 2019 | 10 | 2019 |
A spontaneous mouse deletion in Mctp1 uncovers a long-range cis-regulatory region crucial for NR2F1 function during inner ear development B Tarchini, C Longo-Guess, C Tian, ALD Tadenev, N Devanney, ... Developmental biology 443 (2), 153-164, 2018 | 9 | 2018 |